lipofuscinoses neuronal ceroid (NCLs) is the most common neurodegenerative disorder-onset period marked by autosomal recessive inheritance, epileptic seizures, progressive psychomotor damage, visual failure, and early death. At least seven subtypes of NCLs time-onset have been identified from which the final form of infantile-onset (LINCLs) is genetically most heterogeneous with four genes that underlie identified.
A variant form of LINCL (vLINCL) present in patients Turkey has been regarded as a clinical entity and different genetic (CLN7). However, we have recently demonstrated that mutations in the gene CLN8 account for a subset of Turkey vLINCL. Towards identifying genes CLN7 us here filtered NCL loci known homozygosity in a family of nine Turkish vLINCL.
This locus is issued in seven families who may represent the ‘true’ Turkish vLINCL. In two families, we identified two novel homozygous mutation in the gene CLN6: base substitution intronic (c.542 + 5G> T) affects splicing of the transcript and nonsense mutation (c.663C> G) creates a stop codon at Tyrosine 221. These data indicate that CLN6 mutations, other than those of CLN8, should be considered as a diagnostic alternative in patients Turkey vLINCL. The genetic background of the ‘true’ Turkish vLINCL, CLN7, still to be defined.
di-Sodium Dihydrogen Ethylenediaminetetraacetate Dihydrate |
15130-95 |
NACALAI TESQUE |
500G |
EUR 50.4 |
di-Sodium Dihydrogen Ethylenediaminetetraacetate Dihydrate |
09592-45 |
NACALAI TESQUE |
500G |
EUR 67.2 |
Calcium di-Sodium Ethylenediaminetetraacetate |
15116-82 |
NACALAI TESQUE |
25G |
EUR 14 |
di-Sodium Zinc Ethylenediaminetetraacetate |
15126-52 |
NACALAI TESQUE |
25G |
EUR 13.3 |
EDTA, Disodium Salt, Dihydrate, (Ethylenediaminetetraacetic Acid), 1kg |
PC0706-1kg |
Vivantis |
each |
Ask for price |
EDTA, Disodium Salt, Dihydrate, (Ethylenediaminetetraacetic Acid), 500g |
PC0706-500g |
Vivantis |
each |
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Copper(Ⅱ) di-Sodium Ethylenediaminetetraacetate |
15119-52 |
NACALAI TESQUE |
25G |
EUR 18.9 |
Manganese(Ⅱ) di-Sodium Ethylenediaminetetraacetate |
15123-82 |
NACALAI TESQUE |
25G |
EUR 88.2 |
Ethylenediaminetetraacetic acid disodium salt dihydrate Reagent Grade |
E08850 |
Pfaltz & Bauer |
100G |
EUR 119.52 |
|
Description: CAS N° 139-33-3 |
Magnesium di-Sodium Ethylenediaminetetraacetate Tetrahydrate |
15122-92 |
NACALAI TESQUE |
25G |
EUR 15.4 |
di-Potassium Dihydrogen Ethylenediaminetetraacetate |
15108-05 |
NACALAI TESQUE |
500G |
EUR 81.2 |
di-Potassium Dihydrogen Ethylenediaminetetraacetate |
15108-92 |
NACALAI TESQUE |
25G |
EUR 12.46 |
0.1mol/l-di-Sodium Dihydrogen Ethylenediaminetetraacetate Solution |
37310-55 |
NACALAI TESQUE |
500ML |
EUR 18.9 |
0.01mol/l-di-Sodium Dihydrogen Ethylenediaminetetraacetate Solution |
37311-45 |
NACALAI TESQUE |
500ML |
EUR 18.9 |
0.2mol/l-di-Sodium Dihydrogen Ethylenediaminetetraacetate Solution |
37336-35 |
NACALAI TESQUE |
500ML |
EUR 25.9 |
0.02mol/l-di-Sodium Dihydrogen Ethylenediaminetetraacetate Solution |
37337-25 |
NACALAI TESQUE |
500ML |
EUR 19.6 |
0.05mol/l-di-Sodium Dihydrogen Ethylenediaminetetraacetate Solution |
37341-55 |
NACALAI TESQUE |
500ML |
EUR 19.6 |
tetra-Sodium Ethylenediaminetetraacetate |
15114-02 |
NACALAI TESQUE |
25G |
EUR 13.3 |
tetra-Sodium Ethylenediaminetetraacetate |
15114-15 |
NACALAI TESQUE |
500G |
EUR 35.7 |
Iron(Ⅲ) Monosodium Ethylenediaminetetraacetate |
15120-12 |
NACALAI TESQUE |
25G |
EUR 15.4 |
Iron(Ⅲ) Monosodium Ethylenediaminetetraacetate |
15120-25 |
NACALAI TESQUE |
500G |
EUR 48.65 |
tri-Sodium Hydrogen Ethylenediaminetetraacetate |
15113-12 |
NACALAI TESQUE |
25G |
EUR 10.85 |
tri-Sodium Hydrogen Ethylenediaminetetraacetate |
15113-25 |
NACALAI TESQUE |
500G |
EUR 65.8 |
tri-Potassium Hydrogen Ethylenediaminetetraacetate |
15109-82 |
NACALAI TESQUE |
25G |
EUR 22.4 |
Ethylenediaminetetraacetic acid trisodium salt dihydrate 98% |
E08540 |
Pfaltz & Bauer |
100G |
EUR 140 |
|
Description: CAS N° 150-38-9 |
Ethylenediaminetetraacetic acid manganese disodium salt trihydrate |
20-abx184692 |
Abbexa |
-
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|
|
|
Ethylenediamine-N,N,N’,N’-tetraacetic Acid Disodium Dihydrate |
E917735 |
Toronto Research Chemicals |
10g |
EUR 253 |
|
Description: 6381-92-6 |
Ethylenediaminetetraacetic acid (trisodium salt) |
HY-B1009 |
MedChemExpress |
1g |
EUR 43.29 |
Description: Ethylenediaminetetraacetic acid trisodium salt (EDTA trisodium salt; Trisodium EDTA) is a kind of metal chelating agent (binds to bivalent and trivalent metal cations, including calcium). Ethylenediaminetetraacetic acid trisodium salt has antibacterial, anti-inflammatory, antioxidant, anti-hypercalcemia and anticoagulant activities. Ethylenediaminetetraacetic acid trisodium salt decreases the metal ion-catalyzed oxidative damage to proteins, and allows maintenance of reducing environment during protein purification. Ethylenediaminetetraacetic acid trisodium salt can alleviate the liver fibrosis. Ethylenediaminetetraacetic acid can be used for coronary artery disease and neural system disease research[1][2][3][4][5][6][7]. |
Ethylenediaminetetraacetic acid trisodium salt |
T0423-10mg |
TargetMol Chemicals |
10mg |
Ask for price |
|
Description: Ethylenediaminetetraacetic acid trisodium salt |
Ethylenediaminetetraacetic acid trisodium salt |
T0423-1g |
TargetMol Chemicals |
1g |
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|
Description: Ethylenediaminetetraacetic acid trisodium salt |
Ethylenediaminetetraacetic acid trisodium salt |
T0423-1mg |
TargetMol Chemicals |
1mg |
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|
Description: Ethylenediaminetetraacetic acid trisodium salt |
Ethylenediaminetetraacetic acid trisodium salt |
T0423-50mg |
TargetMol Chemicals |
50mg |
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|
Description: Ethylenediaminetetraacetic acid trisodium salt |
Ethylenediaminetetraacetic acid trisodium salt |
T0423-5mg |
TargetMol Chemicals |
5mg |
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|
Description: Ethylenediaminetetraacetic acid trisodium salt |
Ethylenediaminetetraacetic acid trisodium salt solution |
MBS576716-1g |
MyBiosource |
1g |
EUR 145 |
Ethylenediaminetetraacetic acid trisodium salt solution |
MBS576716-500mg |
MyBiosource |
500mg |
EUR 145 |
Ethylenediaminetetraacetic acid trisodium salt solution |
MBS576716-5x1g |
MyBiosource |
5x1g |
EUR 505 |
(S)-1-(p-Bromoacetamidobenzyl)ethylenediaminetetraacetic Acid (~80%) |
B679000 |
Toronto Research Chemicals |
25mg |
EUR 193 |
|
Description: 81677-64-7 |
rac (Aminomethyl)ethylenediaminetetraacetic Acid tetra-(t-Butyl Ester) |
A616160 |
Toronto Research Chemicals |
250mg |
EUR 201 |
|
Description: 1391052-55-3 |
4-Aminobenzyl Ethylenediaminetetraacetic Acid, Tetra(t-butyl) Ester |
MBS6078540-10mg |
MyBiosource |
10(mg |
EUR 505 |
4-Aminobenzyl Ethylenediaminetetraacetic Acid, Tetra(t-butyl) Ester |
MBS6078540-5x10mg |
MyBiosource |
5x10mg |
EUR 2125 |
rac (Aminomethyl)ethylenediaminetetraacetic Acid tetra-(t-Butyl Ester) |
MBS6034066-25mg |
MyBiosource |
25(mg |
EUR 610 |
rac (Aminomethyl)ethylenediaminetetraacetic Acid tetra-(t-Butyl Ester) |
MBS6034066-5x25mg |
MyBiosource |
5x25mg |
EUR 2600 |
(S)-1-(p-Bromoacetamidobenzyl)ethylenediaminetetraacetic Acid (BABE) |
MBS6041271-5mg |
MyBiosource |
5(mg |
EUR 545 |
(S)-1-(p-Bromoacetamidobenzyl)ethylenediaminetetraacetic Acid (BABE) |
MBS6041271-5x5mg |
MyBiosource |
5x5(mg |
EUR 2310 |
(S)-1-(4-Aminoxyacetamidobenzyl)ethylenediaminetetraacetic Acid (AABE) |
MBS6025607-5mg |
MyBiosource |
5(mg |
EUR 545 |
(S)-1-(4-Aminoxyacetamidobenzyl)ethylenediaminetetraacetic Acid (AABE) |
MBS6025607-5x5mg |
MyBiosource |
5x5(mg |
EUR 2310 |
EDTA Iron(III) sodium salt (Ethylenediaminetetraacetic acid iron(III), Edathamil, Komplexon II) |
MBS635476-50g |
MyBiosource |
50g |
EUR 345 |
EDTA Iron(III) sodium salt (Ethylenediaminetetraacetic acid iron(III), Edathamil, Komplexon II) |
MBS635476-5x50g |
MyBiosource |
5x50g |
EUR 1410 |
4-(N-Boc-aminoxyacetamido)benzyl Ethylenediaminetetraacetic Acid, Tetra(t-butyl) Ester |
MBS6118728-5mg |
MyBiosource |
5(mg |
EUR 525 |
4-(N-Boc-aminoxyacetamido)benzyl Ethylenediaminetetraacetic Acid, Tetra(t-butyl) Ester |
MBS6118728-5x5mg |
MyBiosource |
5x5(mg |
EUR 2210 |
Ethylenediamine-N,N,N’,N’-tetraacetic Acid Calcium Disodium Hydrate |
E917590 |
Toronto Research Chemicals |
100g |
EUR 161 |
|
Description: 23411-34-9 |
Ethylenediamine dihydroiodide |
E08440 |
Pfaltz & Bauer |
500G |
EUR 2053.6 |
Description: CAS N° 5700-49-2 |
Ethylenediamine dihydrochloride |
40000027-1 |
Bio-WORLD |
100 g |
EUR 29.69 |
|
Ethylenediamine dihydrochloride |
40000027-2 |
Bio-WORLD |
500 g |
EUR 98.98 |
|
N-(1-Naphthyl)ethylenediamine dihydrochl |
RM1073-25G |
EWC Diagnostics |
1 unit |
EUR 69.21 |
Description: N-(1-Naphthyl)ethylenediamine dihydrochl |
N-(1-Naphthyl)ethylenediamine dihydrochl |
RM1073-5G |
EWC Diagnostics |
1 unit |
EUR 15.42 |
Description: N-(1-Naphthyl)ethylenediamine dihydrochl |
N-(1-Naphthyl)-ethylenediamine dihydrochloride |
NB0650 |
Bio Basic |
10g |
EUR 84.01 |
|
Ethylenediamine dihydrochloride_x000D__x000D__x000D_ |
E08430 |
Pfaltz & Bauer |
5G |
EUR 436.97 |
Description: CAS N° 333-18-6 |
CTP disodium dihydrate |
MBS5758743-100mg |
MyBiosource |
100mg |
EUR 320 |
CTP disodium dihydrate |
MBS5758743-10mg |
MyBiosource |
10mg |
EUR 160 |
CTP disodium dihydrate |
MBS5758743-25mg |
MyBiosource |
25mg |
EUR 200 |
CTP disodium dihydrate |
MBS5758743-50mg |
MyBiosource |
50mg |
EUR 250 |
CTP disodium dihydrate |
MBS5758743-5mg |
MyBiosource |
5mg |
EUR 145 |
CTP disodium dihydrate |
MBS3611149-5mg |
MyBiosource |
5mg |
EUR 200 |
CTP disodium dihydrate |
MBS3611149-5x5mg |
MyBiosource |
5x5mg |
EUR 580 |
CTP disodium dihydrate |
T7881-10mg |
TargetMol Chemicals |
10mg |
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|
Description: CTP disodium dihydrate |
CTP disodium dihydrate |
T7881-1g |
TargetMol Chemicals |
1g |
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|
Description: CTP disodium dihydrate |
CTP disodium dihydrate |
T7881-1mg |
TargetMol Chemicals |
1mg |
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|
Description: CTP disodium dihydrate |
CTP disodium dihydrate |
T7881-50mg |
TargetMol Chemicals |
50mg |
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|
Description: CTP disodium dihydrate |
CTP disodium dihydrate |
T7881-5mg |
TargetMol Chemicals |
5mg |
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|
Description: CTP disodium dihydrate |
N-(1-Naphthyl)Ethylenediamine Dihydrochloride (NEDA) extrapure AR, ACS, 98% |
61166 |
Sisco Laboratories |
5 Gms |
EUR 5.78 |
|
Description: Part B |
E.D.T.A., disodium salt, dihydrate |
MB011-1KG |
EWC Diagnostics |
1 unit |
EUR 26.7 |
Description: E.D.T.A., disodium salt, dihydrate |
E.D.T.A., disodium salt, dihydrate |
MB011-500G |
EWC Diagnostics |
1 unit |
EUR 15.27 |
Description: E.D.T.A., disodium salt, dihydrate |
E.D.T.A., disodium salt dihydrate |
PCT0105-100G |
EWC Diagnostics |
1 unit |
EUR 6.93 |
Description: E.D.T.A., disodium salt dihydrate |
E.D.T.A., disodium salt dihydrate |
PCT0105-1KG |
EWC Diagnostics |
1 unit |
EUR 31.97 |
Description: E.D.T.A., disodium salt dihydrate |
E.D.T.A., disodium salt dihydrate |
PCT0105-500G |
EWC Diagnostics |
1 unit |
EUR 17.75 |
Description: E.D.T.A., disodium salt dihydrate |
E.D.T.A., disodium salt dihydrate |
PCT0105-5KG |
EWC Diagnostics |
1 unit |
EUR 127.76 |
Description: E.D.T.A., disodium salt dihydrate |
ADP disodium salt, dihydrate |
MB191-1G |
EWC Diagnostics |
1 unit |
EUR 14.92 |
Description: ADP disodium salt, dihydrate |
ADP disodium salt, dihydrate |
MB191-5G |
EWC Diagnostics |
1 unit |
EUR 72.95 |
Description: ADP disodium salt, dihydrate |
Nitroprusside (disodium dihydrate) |
HY-A0119 |
MedChemExpress |
500mg |
EUR 59.52 |
Description: Nitroprusside disodium dehydrate (Sodium nitroprusside dihydrate) is a vasodilator that available for the research of acute hypertension, heart failure. Nitroprusside disodium dehydrate induces autophagy in glutathione-depleted osteoblasts. Nitroprusside disodium dehydrate acts as a nitric oxide (NO) donor in a rat intestinal ischemia reperfusion model[1][2][3][4]. |
Nitroprusside disodium dihydrate |
T6991-10mg |
TargetMol Chemicals |
10mg |
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|
Description: Nitroprusside disodium dihydrate |
Nitroprusside disodium dihydrate |
T6991-1g |
TargetMol Chemicals |
1g |
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|
Description: Nitroprusside disodium dihydrate |
Nitroprusside disodium dihydrate |
T6991-1mg |
TargetMol Chemicals |
1mg |
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|
Description: Nitroprusside disodium dihydrate |
Nitroprusside disodium dihydrate |
T6991-50mg |
TargetMol Chemicals |
50mg |
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|
Description: Nitroprusside disodium dihydrate |
Nitroprusside disodium dihydrate |
T6991-5mg |
TargetMol Chemicals |
5mg |
Ask for price |
|
Description: Nitroprusside disodium dihydrate |
EDTA Disodium Salt Dihydrate |
40500012-1 |
Bio-WORLD |
500 g |
EUR 69.53 |
|
EDTA Disodium Salt Dihydrate |
40500012-2 |
Bio-WORLD |
1 kg |
EUR 114.8 |
|
EDTA Disodium Salt Dihydrate |
40500012-3 |
Bio-WORLD |
2.5 kg |
EUR 241.35 |
|
EDTA Disodium Salt Dihydrate |
40500012-4 |
Bio-WORLD |
5 kg |
EUR 411.26 |
|
EDTA Disodium Salt Dihydrate |
40500012-5 |
Bio-WORLD |
10 kg |
EUR 800.11 |
|
EDTA, Disodium Dihydrate Salt |
20-147 |
Genesee Scientific |
500g/Unit |
EUR 73.04 |
Description: Ultra Pure Grade |
EDTA, Disodium Salt, Dihydrate |
A2503-1KG |
Biomatik Corporation |
1KG |
EUR 46.2 |
Description: Biotechnology |
EDTA, Disodium Salt, Dihydrate |
A2503-500G |
Biomatik Corporation |
500G |
EUR 26.4 |
Description: Biotechnology |
EDTA, Disodium Salt, Dihydrate |
A2503-5KG |
Biomatik Corporation |
5KG |
EUR 189.2 |
Description: Biotechnology |
EDTA, Disodium Salt, Dihydrate |
CH032 |
ABM |
500 g |
EUR 195.6 |
EDTA, Disodium Salt, Dihydrate |
CH033 |
ABM |
1.0 kg |
EUR 130 |
Description: A reversible metalloprotease inhibitor useful for chelating metal ions. |
EDTA, Disodium Salt, Dihydrate |
CH034 |
ABM |
2.5 kg |
EUR 400.8 |
EDTA, disodium salt, dihydrate |
EB0185 |
Bio Basic |
500g |
EUR 84.01 |
|
EDTA disodium salt dihydrate |
GRM1195-100G |
EWC Diagnostics |
1 unit |
EUR 6.93 |
Description: EDTA disodium salt dihydrate |
EDTA disodium salt dihydrate |
GRM1195-1KG |
EWC Diagnostics |
1 unit |
EUR 25.12 |
Description: EDTA disodium salt dihydrate |
EDTA disodium salt dihydrate |
GRM1195-500G |
EWC Diagnostics |
1 unit |
EUR 13.97 |
Description: EDTA disodium salt dihydrate |
EDTA Disodium Salt Dihydrate |
MBS635343-100g |
MyBiosource |
100g |
EUR 155 |
EDTA Disodium Salt Dihydrate |
MBS635343-1kg |
MyBiosource |
1kg |
EUR 320 |
EDTA Disodium Salt Dihydrate |
MBS635343-25kg |
MyBiosource |
2.5kg |
EUR 690 |
EDTA Disodium Salt Dihydrate |
MBS635343-500g |
MyBiosource |
500g |
EUR 260 |
EDTA Disodium Salt Dihydrate |
MBS635343-5kg |
MyBiosource |
5kg |
EUR 1020 |
EDTA, Disodium Salt, Dihydrate |
MBS4156372-500g |
MyBiosource |
500g |
EUR 260 |
EDTA, Disodium Salt, Dihydrate |
MBS4156372-5x500g |
MyBiosource |
5x500g |
EUR 920 |
EDTA, Disodium Salt, Dihydrate |
MBS4156373-1kg |
MyBiosource |
1kg |
EUR 285 |
EDTA, Disodium Salt, Dihydrate |
MBS4156373-5x1kg |
MyBiosource |
5x1kg |
EUR 1095 |
EDTA, Disodium Salt, Dihydrate |
MBS4156374-25kg |
MyBiosource |
2.5kg |
EUR 465 |
EDTA, Disodium Salt, Dihydrate |
MBS4156374-5x25kg |
MyBiosource |
5x2.5kg |
EUR 1705 |
EDTA Disodium Salt Dihydrate 0.057M |
40500040-1 |
Bio-WORLD |
500 mL |
EUR 25.2 |
EDTA Disodium Salt Dihydrate 0.057M |
40500040-2 |
Bio-WORLD |
1 L |
EUR 42.6 |
EDTA Disodium Salt Dihydrate 0.057M |
40500040-3 |
Bio-WORLD |
4 L |
EUR 110.75 |
Tartaric acid disodium dihydrate |
C6836-1000 |
ApexBio |
1g |
EUR 48 |
|
Description: Metabolic Enzyme/Protease|Phosphatase |
Tartaric acid disodium dihydrate |
C6836-500 |
ApexBio |
500mg |
EUR 40 |
|
Description: Metabolic Enzyme/Protease|Phosphatase |